Scimitar Syndrome or Halasz Syndrome

ELMouden H, Nashi L, Salam S, Chbani K, Laoudiyi D and Ouzidane L

Published on: 2022-06-09

Abstract

Scimitar syndrome or Felson's vein-lobar syndrome is a very rare condition characterized by a combination of cardiopulmonary abnormalities including abnormal right pulmonary venous return, most often located in the inferior vena cava. We here report an original observation of a nine-month-old female infant who presented with acute dyspnea in an endemic period. Symptomatic treatment for bronchiolitis was initiated, without success, with persistent respiratory distress. The diagnosis was suspected on chest X-ray and confirmed on CT scan which showed a single large right pulmonary vein draining into the right atrium associated with dextrocardia and pulmonary sequestration.