A Case of Recurrent Kikuchi-Fujimoto Disease

Noor MAP, Ismail M and Koka M

Published on: 2022-07-13


Kikuchi-Fujimoto disease or necrotising histiocytic lymphadenitis is a rare non-malignant immune mediated condition that presents with cervical lymphadenopathy, upper respiratory tract symptoms, low grade fever, night sweats and weight loss in young females. Although mostly self-resolving after months of onset, recurrences have been reported increasingly, with certain specific factors predicting frequent relapse. It closely mimics lymphoproliferative disorders and has been reported as a harbinger of autoimmune diseases like SLE. Here we describe a case of a young female with past history of KD who presented with painful cervical lymphadenopathy, fever, cough, along with leukopenia and splenomegaly with node biopsy revealing KD, who was treated with a prolonged course of steroids for the relapsing disease.